Huntington’s disease by Ray Sahelian, M.D.
Huntingtons disease, along with Alzheimer's and Parkinson's, belong to the family of neurodegenerative diseases caused by protein misfolding. The incurable disease is hereditary and has a prevalence of 1 in every 15,000 people. In Germany, about 8,000 cases are currently known, in the UK the figure is reported to be about 5,000, and in the US the figure is about 30,000.
Huntington's Disease Symptoms
The disease is characterize by jerky, uncontrolled movements, an unsteady gait
and grimaces leading to its original common name of Huntington's chorea (from
the ancient Greek for “dance”).
Huntington’s disease Gene
In 1993, scientists discovered the gene that encodes the mutant protein, the
so-called huntingtin protein. A mutation in this protein results in elongation
of parts of the protein called polyglutamine chains, which cause the overall
huntingtin protein to lose its normal structure. These mutant proteins can not
be disposed of by the body and accumulate in the brain of sufferers, eventually
being toxic to the nerve cells in the brain.
Green Tea for Huntington's Disease
The green tea extract, epigallocatechin gallate (
EGCG ), may slow the
accumulation of proteins that cause Huntington’s disease. The new research, led
by Professor Erich Wanker from the Max Delbrück Center for Molecular Medicine
Berlin-Buch (MDC), looked at the effect on EGCG on the aggregation of these
mutant proteins in vitro, and found that the green tea extract could interfere
with the very early events of this process. The research is published in the
September issue journal Human Molecular Genetics (Vol. 15, pp. 2743-2751).
Professor Wanker's group used laboratory-based experiments to show that the
green tea extract inhibited misfolding of the huntingtin protein in vitro, as
well as using fruit flies genetically modified to over-express the mutant
protein. The latter experiments showed that the degeneration of the flies'
photoreceptor and motor function improved. Further research is needed,
particular to discern if the bioactive doses needed to produce these protective
effects could be obtained from drinking green tea, or by taking supplements.
Huntington's disease questions
There is not a lot of information available to
me on my Huntington disease. I have been taking Gingko Biloba & 5HTP 50mg's -
these have helped me. I am just wondering if there are anything other
supplements I should know about.
A. Only green tea or egcg that we know of thus far.